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An Unusual Case of Presacral Carcinoid Tumor and the Approach of Management

Joelle FS Wong, Ching Ching Melissa Teo

Abstract


Introduction: Gut derived neuroendocrine tumors (NETs) are a heterogenous group of tumors classified as Gastroenteropancreatic (GEP) NETs. These tumors can be found along the gastrointestinal tract from the foregut, mid, to the hindgut. They are referred to as carcinoid tumors due to their potential to secrete bioactive hormones.

Presacral tumors are a subset of GEP NETs that are histologically similar. They are uncommon tumors that are found at the presacral space and are often clinically silent with no associated carcinoid syndrome.
Presentation of Case: We report a case of 49 year old female who was diagnosed with a presacral carcinoid tumor. Her initial presentation, investigations that led up to the final diagnosis and management of the tumor are discussed.
Conclusion: Presacral carcinoid tumors are NETs that are clinically and histologically similar to GEPs arising from the colon or rectum. Management of such tumors is often surgical resection of localized disease with a long follow-up of surveillance to detect recurrence and metastasis.

Keywords


Carcinoid tumour; Presacral; Tailgut cyst; Neuroendocrine; Gastroenteropancreatic

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References


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