Primary penoscrotal myxoid chondrosarcomas
Introduction: Extraskeletal myxoid chondrosarcoma (EMC) is a rare tumor of cartilaginous origin, most commonly located in the extremities that usually presents as a slow growing mass in fifth to sixth decades of life. Primary genitourinary tract involvement is extremely rare; about ten cases reported so far and due to such a low incidence, therapeutic approach is very challenging
Case presentation: We report 2 year follow-up of a 38-year-old man with penoscrotal EMC that has been managed by complete tumor excision.
Conclusion: Wide excision seems to be the best treatment. Our patient had no signs of local recurrence or metastasis during 4 years of follow up period.
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