Cover Image

Extraosseous Renal Ewing Sarcoma: The “Blue” Tumour in kidney

Ng Han Kun, Shankaran Thevarajah

Abstract


Introduction: Primary Ewing sarcoma (ES) is a distinctly rare tumour in the kidney and very limited cases were reported till date.

Case Presentation: Herein, we report a case of right renal ES in a young boy who presented with bleeding right renal tumour and underwent emergency right radical nephrectomy. Tumour cells are strongly positive for CD99 and FLI-1, thus confirming the diagnosis.

Conclusion: Therefore, this entity should always be one of the differential diagnosis while dealing renal masses in young population.


Keywords


Renal;extraosseus; Ewing’s sarcoma; blue tumour; CD-99, FLI-1

References


Almeida MF, Patnana M, Korivi BR, et al. Ewing Sarcoma of the kidney: A rare entity. Case Rep Radiol.2014, 2014:283902

Riggi N, Stamenkovic I. The Biology of Ewing Sarcoma. Cancer Lett. 2007, 254: 1-10

Seemayer TA, Thelmo WL, Bolande RP, et al. Peripheral neuroectodermaltumors. PerspectPediatrPatho. 1975, l 2:151-172

Pernick N. CD99. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/cdmarkerscd99.html. Accessed July 13th, 2019

Stuart L. FLI1. PathologyOutlines.com website. https://www.pathologyoutlines.com/topic/stainsfli1.html. Accessed July 13th, 2019

Ekram T, Elsayes KM, Cohan RH, and Francis IR. Computed tomography and magnetic resonance features of renal ewing sarcoma. ActaRadiologica. 2008, 49(9):1085-1090

Lalwani N, Prasad SR, Vikram R, Katabathina V, Shanbhogue A, and Restrepo C. Pediatric and adult primary sarcomas of the kidney: a cross-sectional imaging review. ActaRadiologica. 2011, 52(4):448-457

Ellinger J, Bastian PJ, Hauser S, Biermann K, and Müller SC. Primitive neuroectodermaltumor: rare, highly aggressive differential diagnosis in urologic malignancies. Urology. 2006, 68( 2):257-262

Angel JR, Alfred A, Sakhuja A et al. Ewing's sarcoma of the kidney.International Journal of Clinical Oncology. 2010, 15:314-318

Venkitaraman R, Mukkunda R, Thway K et al. Primary adult renal Ewing's Sarcoma: a rare entity. Sarcoma. 2009, 2009:504654

Fergany F, Dhar N, Budd GT, Skacel M, and Garcia J. Primary extraosseousewing sarcoma of the kidney with level III inferior vena cava thrombus. Clinical Genitourinary Cancer. 2009, 7(3):E95-E97

Rizzo D, Barone G, Ruggiero A et al. Massive venous thrombosis of inferior vena cava as primary manifestation of renal Ewing's sarcoma. Clinical Nephrology. 2011, 75(6) :560-564

Jimenez RE, Folpe AL, Lapham RL et al. Primary Ewing's sarcoma/primitive neuroectodermaltumor of the kidney: a clinicopathologic and immunohistochemical analysis of 11 cases. American Journal of Surgical Pathology. 2002, 26(3):320-328

Risi E, Iacovelli R, Altavilla A, et al. Clinical and pathological features of primary neuroectodermaltumor/Ewing Sarcoma of the kidney. Urology. 2013, 82:382-386

Hakky TS, Gonzalvo AA, Lockhart JL, et al. Primary Ewing Sarcoma of the kidney: A symptomatic presentation and review of the literature. TherAdv Urol. 2013, 5:153-159


Full Text: PDF

Refbacks

  • There are currently no refbacks.


AJCC-REP (ISSN 2572-5742)Copyright © 2012-2019. All rights reserved. Published by Ivy Union Publishing, 3204 Valley Rush Dr, Apex, North Carolina 27502, United States