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Management of Secondary Hemophagocytosis Lymphohistiocytosis with Severe Liver Dysfunction

Rohit Kumar


Introduction:Hemophagocytosis Lymphohistiocytosis (HLH) is a syndrome of inappropriate hyperimmune response. 

Presentation of Case:We present a case of secondary HLH associated with systemic lupus erythematous (SLE) and liver dysfunction.

Conclusion:This case report focuses on the diagnostic dilemmas with HLH and an individualized treatment approach to the patient.


Hemophagocytosis Lymphohistiocytosis; liver dysfunction

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