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Extra-skeletal Ewing’s Sarcoma of Caecum Causing Intussusception: First such Reported Case

Paritosh Gupta, Dhruv Nayan Kundra, Amanpriya Khanna, Aakanksha Aggarwal


Introduction: Ewing’s sarcoma is a tumor of primitive cells which primarily affects long bones. Extra-skeletal Ewing’s sarcoma has been rarely reported in small bowel. Its presentation can be varied but it is an extremely unlikely cause of an Ileo-Colic Intussusception as seen in present case.

Case Presentation: A 32 years old male patient presented with symptoms suggestive of bowel obstruction. CT scan was suggestive of Ileo-colic intussusception. Patient underwent diagnostic laparoscopy and right hemicolectomy. Histopathology examination of specimen revealed Ewing sarcoma of colon.

Conclusion: Extra-skeletal Ewing’s sarcoma is a rare entity. To the best of our knowledge this is the first reported case in English literature, of a Caecal Ewing’s sarcoma causing Intussusception. Further study of such cases may help in better understanding and establishing treatment protocol for this condition.


Extra-skeletal Ewing’s Sarcoma; Caecal; Intussusception

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